[Thrombotic microangiopathies]
Research output: Contribution to journal › Journal article › Research › peer-review
The thrombotic microangiopathic diseases, which include acquired and congenital TTP and HUS, are most frequently acute disease entities. Untreated, these diseases are associated with a lethal course in many cases. Deficiency of the von Willebrand cleaving enzyme, ADAMTS13, is a decisive pathophysiological defect in most cases of thrombotic microangiopathic diseases. Early recognition and a secure distinction from other conditions that resemble TMA diseases is essential in order to institute adequate treatment and to obtain a favourable outcome in terms of both survival and development of serious sequelae
Udgivelsesdato: 2009/11/30
Udgivelsesdato: 2009/11/30
Original language | Danish |
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Journal | Ugeskrift for læger |
Volume | 171 |
Issue number | 49 |
Pages (from-to) | 3614-3620 |
Number of pages | 6 |
ISSN | 0041-5782 |
Publication status | Published - 2009 |
ID: 19797819