Behavioral variant of frontotemporal dementia mimicking Huntington's disease
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Behavioral variant of frontotemporal dementia mimicking Huntington's disease. / Nielsen, T Rune; Bruhn, Peter; Nielsen, Jørgen E; Hjermind, Lena E.
I: International Psychogeriatrics, Bind 22, Nr. 4, 2010, s. 674-7.Publikation: Bidrag til tidsskrift › Tidsskriftartikel › Forskning › fagfællebedømt
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TY - JOUR
T1 - Behavioral variant of frontotemporal dementia mimicking Huntington's disease
AU - Nielsen, T Rune
AU - Bruhn, Peter
AU - Nielsen, Jørgen E
AU - Hjermind, Lena E
PY - 2010
Y1 - 2010
N2 - Behavioral changes and cognitive decline are the core clinical manifestations in the behavioral variant of frontotemporal dementia (bv-FTD). The behavioral changes may include characteristic stereotypic movements. These movements, although without clear purpose, are not involuntary. Involuntary movements are usually not seen in FTD.Two patients with involuntary choreoathetoid movements but otherwise presenting a bv-FTD-phenotype were referred and Huntington's disease (HD) was suspected. The diagnoses of bv-FTD were made after comprehensive assessment and exclusion of other diagnoses, including HD and Huntington's disease-like (HDL) phenotypes. Although a definite diagnosis will require neuropathological confirmation, we conclude that a HDL phenotype may be part of the clinical spectrum of the bv-FTD phenotype.
AB - Behavioral changes and cognitive decline are the core clinical manifestations in the behavioral variant of frontotemporal dementia (bv-FTD). The behavioral changes may include characteristic stereotypic movements. These movements, although without clear purpose, are not involuntary. Involuntary movements are usually not seen in FTD.Two patients with involuntary choreoathetoid movements but otherwise presenting a bv-FTD-phenotype were referred and Huntington's disease (HD) was suspected. The diagnoses of bv-FTD were made after comprehensive assessment and exclusion of other diagnoses, including HD and Huntington's disease-like (HDL) phenotypes. Although a definite diagnosis will require neuropathological confirmation, we conclude that a HDL phenotype may be part of the clinical spectrum of the bv-FTD phenotype.
U2 - 10.1017/S1041610210000098
DO - 10.1017/S1041610210000098
M3 - Journal article
C2 - 20170589
VL - 22
SP - 674
EP - 677
JO - International Psychogeriatrics
JF - International Psychogeriatrics
SN - 1041-6102
IS - 4
ER -
ID: 20970016