The cytochrome b p.278Y>C mutation causative of a multisystem disorder enhances superoxide production and alters supramolecular interactions of respiratory chain complexes

Research output: Contribution to journalJournal articlepeer-review

  • Anna Ghelli
  • Concetta V Tropeano
  • Maria Antonietta Calvaruso
  • Alessandra Marchesini
  • Luisa Iommarini
  • Anna Maria Porcelli
  • Claudia Zanna
  • Vera De Nardo
  • Andrea Martinuzzi
  • Flemming Wibrand
  • Vissing, John
  • Ivana Kurelac
  • Giuseppe Gasparre
  • Nur Selamoglu
  • Fevzi Daldal
  • Michela Rugolo
Original languageEnglish
JournalHuman Molecular Genetics
Volume22
Issue number11
Pages (from-to)2141-2151
Number of pages11
ISSN0964-6906
DOIs
Publication statusPublished - 2013

ID: 118102706